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Publikation · PMID 41924323

Hepatic dysfunction, hyperuricemia, and multiple renal cysts in adolescence: A case report with HNF1B deficiency and literature review

Yang Y, Shen Z, Zhang L, Guo W, Gong S, Cai J, Wang J, Yuan S et al.

A case report described an 18-year-old female with a de novo heterozygous 17q12 microdeletion (34807034-36285028) encompassing 17 protein-coding genes, including HNF1B, AATF, and DDX52, presenting with hepatic dysfunction, hyperuricemia, hypomagnesemia, and multiple renal cysts. Whole-exome sequencing with copy number variation verification confirmed the deletion. The findings suggest that whole-exome sequencing is warranted in young patients with early-onset metabolic and renal abnormalities.

Clinical Nephrology. Case Studies, 25. März 2026 | PMID 41924323

Zeitschrift
Clinical Nephrology. Case Studies
DOI
10.5414/CNCS111652
PMID
41924323
Quelle
https://pubmed.ncbi.nlm.nih.gov/41924323/
Zitationen
0